RT Journal A1 Hanzlick R T1 CAse of the month JF Archives of Internal Medicine JO Archives of Internal Medicine YR 1997 FD December 8 VO 157 IS 22 SP 2557 OP 2557 DO 10.1001/archinte.1997.00440430033004 UL http://dx.doi.org/10.1001/archinte.1997.00440430033004 AB A 17-YEAR-OLD girl had a 7-year history of neurologic decline that appeared to be related to a familial degenerative neurologic disorder. She developed chronic malnutrition, decubitus ulcers, marasmus, and repeated episodes of aspiration pneumonia. Her status was placed on do not resuscitate, and she died with a clinical picture of acute respiratory distress syndrome.AUTOPSY FINDINGS  The extent of the autopsy was restricted by the family to removal and examination of the brain and spinal cord. The permit also restricted making incisions into the back or torso. The findings of an extensive neuropathologic workup of the brain were most compatible with a familial olivopontocerebellar atrophy.Based on these findings, a cause of death statement could be prepared as follows:COMMENT  Although the spinal cord may be removed during an autopsy through the foramen magnum using a special tool, the removal may be difficult without causing considerable artifactual damage. Removal of